Coxa Vara
Definition
Coxa Vara is defined as a neck-shaft angle of less than 120 degrees.
Epidemiology
Factor | Details |
---|---|
Incidence | 1 in 25,000 live births |
Gender | Boys = Girls |
Laterality | Left = Right |
Racial Predilection | None |
Bilateral Cases | 30% |
Aetiology
The primary cause is an ossification defect in the infero-medial proximal femoral physis, specifically within Fairbank’s triangle. It is associated with autosomal dominant inheritance and incomplete penetrance.
Types of Coxa Vara
Type | Characteristics |
---|---|
Developmental | Due to primary ossification defect; physis becomes more vertical over time, increasing shear force and leading to physeal separation. |
Congenital | Associated with conditions like Congenital Short Femur (CSF), Proximal Femoral Focal Deficiency (PFFD), fibular hemimelia, etc. |
Acquired | Occurs secondary to conditions like Slipped Upper Femoral Epiphysis (SUFE), Perthes Disease, or Skeletal Dysplasia. |
Clinical Presentation
- Typical Onset: Once a child starts walking, usually before the age of 5.
- Symptoms:
- Trendelenburg gait
- Waddling gait or limp (if bilateral)
- Usually painless
- Prominent trochanter
Imaging Features
- Inverted Y Sign: A pathognomonic feature caused by fragmentation of the infero-medial physis.
- Other Imaging Observations:
- Delayed ossification (may resemble Developmental Dysplasia of the Hip (DDH)).
- Infero-medial quadrant placement of metaphysis.
- Physeal arrest.
- Trochanteric overgrowth.
Management
The treatment approach for coxa vara depends on Hilgenreiner’s Epiphyseal Angle (HEA), which is the angle between the physis and Hilgenreiner’s line.
HEA Angle | Management Strategy |
---|---|
< 45 degrees | Non-operative; often corrects spontaneously |
45-60 degrees | Close observation with serial X-rays |
> 60 degrees | Surgical intervention with osteotomy |
Surgical Approach: Pawels Y-Shaped Osteotomy
- Purpose: Corrects HEA to approximately 16 degrees to reduce shear force on the physis.
- Procedure:
- Calculate osteotomy closing wedge angle as HEA minus 16 degrees.
- Use K-wires to align cuts and saw to perform osteotomy.
- Fixation is achieved with a Tension Band Wire (TBW), blade plate, or locking plate.
- Trochanteric Advancement: Considered if Trendelenburg gait is present.
Complications
- Avascular Necrosis (AVN): Especially common in intracapsular osteotomy.
- Physeal Arrest: Occurs in about 80% of cases.
- Trochanteric Overgrowth: May lead to hip issues.
- Recurrence of Coxa Vara: Noted in approximately 50% of cases after treatment.
Reference
- Lieberman, J. (2009). AAOS Comprehensive Review. American Academy of Orthopaedic Surgeons